Benign Bone Tumours
Classification
Histologic Type
- Osteogenic
- Osteoid Osteoma
- Osteoblastoma
- Chondrogenic
- Chondroma
- Enchondroma
- Chondroblastoma
- Fibrogenic
- Non-Ossifying Fibroma
- Desmoplastic Fibroma
- Chondromyxoid Fibroma
- Cystic
- Unicameral Bone Cyst
- Aneurysmal Bone Cyst
- Unknown origin
- Giant Cell Tumour (GCT)
- Langerhans Cell Histiocytosis (Eosinophilic Granuloma)
Enneking Classification of Benign Bone Tumours
Stage | Activity | Examples |
---|---|---|
1 | Latent | Osteoid Osteoma, Enchondroma, NOF |
2 | Active | Chondroblastoma, UBC |
3 | Aggressive | GCT, ABC |
Osteoid Osteoma
Epidemiology
- Men > Women
- 5–30 years old
Aetiology
- Unknown
Investigations
- X-Ray
- <1 cm nidus with surrounding lucent ring and sclerotic rim
- Extensive sclerosis, especially in the tibia
- Bone Scan
- High uptake
- CT Scan
- Necessary if sclerosis obscures nidus
Presentation
- Night pain
- Long-standing aching pain responsive to NSAIDs, especially aspirin
Location
- Anywhere, but most common:
- Proximal femur
- Tibial diaphysis
- Posterior elements of the spine (painful scoliosis at apex of concavity)
- Can be intra-articular (most common in hip joint)
Pathology
- Uniform osteoid seams
- No pleomorphism or invasion into surrounding bone
Management
- NSAIDs (lesion burns out in 2–3 years)
- RF Ablation under CT guidance (90% cure rate)
- Surgical excision (if other methods fail)
Osteoblastoma
Epidemiology
- Rare
- Commonly occurs in the 20s
Aetiology
- Unknown
Presentation
- Long-standing pain
- Less night pain and less responsive to NSAIDs
- Neurologic symptoms if in the spine
Location
- Long bones (metaphysis or diaphysis)
- Pelvis
- Proximal femur
- Posterior elements of the spine (scoliosis)
Pathology
- Similar to Osteoid Osteoma but larger and macroscopic differences
Imaging
- X-Ray
- Sclerotic center with surrounding expanding lucent area
- More extensive lucency than Osteoid Osteoma
- May mimic malignant lesions
- CT Scan
- Evaluates true extent
- Bone Scan
- High uptake
Differential Diagnosis
- Osteoid Osteoma, Osteosarcoma, ABC, GCT
- 10–40% contain an ABC
Management
- Surgical due to locally aggressive nature
- Marginal resection
- Curettage and grafting
Paraosteal Osteoma
- Rare, benign, self-limiting tumor
- Grows on the bone surface like pedunculated osteochondroma
- Associated with Gardener’s syndrome (multiple osteomas, colonic polyps, fibromatosis)
Histology
- Mature lamellar bone
Bone Islands (Enostosis)
Aetiology
- Focal failure of endochondral ossification
Imaging
- Dense cortical, well-demarcated intramedullary lesion
- Low signal on T1 and T2 MRI, no surrounding edema
Management
- None if asymptomatic
- Surveillance or biopsy if diagnosis is unclear
Osteopikilosis
- Hereditary condition with multiple bone islands
- Autosomal dominant
- Associated conditions: syndactyly, dwarfism
Enchondroma
Aetiology
- Fragments of epiphyseal cartilage trapped in metaphysis during growth
Location
- Hands, long bones, proximal humerus, distal femur, tibia
Imaging
- Lytic area with chondroid matrix
- Calcification in long bones
- Causes cortical thinning and expansion in hands
Presentation
- Usually asymptomatic, incidental finding
- Pathologic fractures in hands
Management
- Intralesional curettage and grafting if symptomatic and isolated
Associated Conditions
- Ollier’s Disease (20–30% risk of malignant transformation)
- Maffuci’s Syndrome (100% risk of malignant transformation)
Periosteal Chondroma
- Benign tumor on the bone surface under the periosteum
- No malignant potential
Epidemiology
- Rare, occurs between 10–30 years
Management
- Marginal resection if symptomatic
Osteochondroma
Aetiology
- Benign cartilaginous tumor on the bone surface
Epidemiology
- Most common benign bone tumor
- Arises in children, identified in the first two decades of life
Location
- Around knee, proximal humerus, pelvis, posterior spinal elements
Presentation
- Mechanical symptoms from irritation
Management
- Excision if symptomatic or concerns about malignant transformation
- Associated with Multiple Hereditary Exostosis
Chondroblastoma
Epidemiology
- Males > Females
- Found in children and young adults
Location
- Epiphysis or apophysis (e.g., knee, pelvis, proximal humerus)
Imaging
- <4 cm, central in epiphysis with sclerotic rim
Management
- Intralesional curettage and grafting
- Phenol to lower recurrence rate (10%)
Chondromyxoid Fibroma
Epidemiology
- Rare, occurs in the 2nd or 3rd decade
- More common in males
Location
- Metaphyseal regions of long bones (lower limbs)
Management
- Intralesional curettage and grafting
Haemangioma
Epidemiology
- Asymptomatic in most cases
Location
- Vertebral bodies, skull, long bones
Management
- Symptomatic treatment only (e.g., embolization, kyphoplasty)
Non-Ossifying Fibroma (NOF)
Epidemiology
- Common in children aged 5–15 years
Location
- Lower limb long bones, especially distal tibia
Management
- Observation if asymptomatic
- Curettage and grafting if symptomatic
Desmoplastic Fibroma
- Rare, locally aggressive
- Wide excision recommended to minimize recurrence
Langerhans Cell Histiocytosis (Eosinophilic Granuloma)
Epidemiology
- 80% under 20 years, Men > Women
Imaging
- Punched-out lytic lesion, thick periosteal reaction
Management
- Low-dose radiation, curettage, or steroid injection
Cystic Lesions
Unicameral Bone Cyst (UBC)
- Painless, filled with serous fluid
- Pathologic fracture may occur
- Management: Injection, curettage, grafting
Aneurysmal Bone Cyst (ABC)
- Painful, locally aggressive
- May arise de novo or within other lesions
- Management: Curettage and grafting, embolization for pelvic/spinal lesions
Giant Cell Tumour (GCT)
Epidemiology
- Females > Males
- Age: 30–50 years
Features
- Benign but aggressive
- May metastasize to the lung (2%)
Location
- Around the knee, distal radius, spine, pelvis
Imaging
- Eccentric lytic metaphyseal lesion growing into the epiphysis
Management
- Curettage and grafting/cement
- Recurrence rate: 15%
- Embolization for spinal/pelvic lesions